Autoimmune Polyendocrinopathies

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Is a:
  • Disease or Syndrome
Definition:
Autoimmune diseases affecting multiple endocrine organs. Type I is characterized by childhood onset and chronic mucocutaneous candidiasis (candidiasis, chronic mucocutaneous), while type ii exhibits any combination of adrenal insufficiency (addison'S disease), lymphocytic thyroiditis (thyroiditis, autoimmune;), hypoparathyroidism; and gonadal failure. In both types organ-specific antibodies against a variety of endocrine glands have been detected. The type ii syndrome differs from type I in that it is associated with hla-a1 and b8 haplotypes, onset is usually in adulthood, and candidiasis is not present.
Synonyms:
  • Autoimmune Polyendocrinopathies
  • Autoimmune Polyendocrinopathy
  • Autoimmune Polyendocrinopathy Candidiasis Ectodermal Dystrophy
  • Autoimmune Polyendocrinopathy-Candidiasis-Ectodermal-Dystrophies
  • Autoimmune Polyendocrinopathy-Candidiasis-Ectodermal-Dystrophy
  • Autoimmune Polyglandular Syndrome Type I
  • Autoimmune Polyglandular Syndrome Type II
  • Autoimmune Syndrome Type I, Polyglandular
  • Autoimmune Syndrome Type II, Polyglandular
  • Polyendocrinopathy, Autoimmune
  • Polyendocrinopathy-Candidiasis-Ectodermal-Dystrophies, Autoimmune
  • Polyendocrinopathy-Candidiasis-Ectodermal-Dystrophy, Autoimmune
  • Polyglandular Type I Autoimmune Syndrome
  • Polyglandular Type II Autoimmune Syndrome
  • Schmidt Syndrome
  • Schmidt's Syndrome
  • Schmidts Syndrome
  • Syndrome, Schmidt's
Broader Topics:
Narrower Topics:
  • None
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