Ectodermal Dysplasia

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Is a:
  • Congenital Abnormality
  • Disease or Syndrome
Definition:
A group of hereditary disorders involving tissues and structures derived from the embryonic ectoderm. They are characterized by the presence of abnormalities at birth and involvement of both the epidermis and skin appendages. They are generally nonprogressive and diffuse. Various forms exist, including anhidrotic and hidrotic dysplasias, focal dermal hypoplasia, and aplasia cutis congenita.
Synonyms:
  • Anhidrotic Ectodermal Dysplasia
  • Anhidrotic Ectodermal Dysplasias
  • Anhydrotic Ectodermal Dysplasia
  • Anhydrotic Ectodermal Dysplasias
  • Aplasia Cutis Congenita
  • Clouston Syndrome
  • Clouston's Syndrome
  • Cloustons Syndrome
  • Congenital Ectodermal Defect
  • Congenital Ectodermal Defects
  • Defect, Congenital Ectodermal
  • Defects, Congenital Ectodermal
  • Dysplasia, Anhidrotic Ectodermal
  • Dysplasia, Anhydrotic Ectodermal
  • Dysplasia, Ectodermal
  • Dysplasia, Hidrotic Ectodermal
  • Dysplasia, Hydrotic Ectodermal
  • Dysplasias, Anhidrotic Ectodermal
  • Dysplasias, Anhydrotic Ectodermal
  • Dysplasias, Ectodermal
  • Dysplasias, Hidrotic Ectodermal
  • Dysplasias, Hydrotic Ectodermal
  • Ectodermal Defect, Congenital
  • Ectodermal Defects, Congenital
  • Ectodermal Dysplasia, Anhidrotic
  • Ectodermal Dysplasia, Anhydrotic
  • Ectodermal Dysplasia, Hidrotic
  • Ectodermal Dysplasia, Hydrotic
  • Ectodermal Dysplasias
  • Ectodermal Dysplasias, Anhidrotic
  • Ectodermal Dysplasias, Anhydrotic
  • Ectodermal Dysplasias, Hidrotic
  • Ectodermal Dysplasias, Hydrotic
  • Hidrotic Ectodermal Dysplasia
  • Hidrotic Ectodermal Dysplasias
  • Hydrotic Ectodermal Dysplasia
  • Hydrotic Ectodermal Dysplasias
  • Syndrome, Clouston's
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