Basal Cell Nevus Syndrome

Overview

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Is a:

Neoplastic Process

Definition:

Hereditary disorder consisting of multiple basal cell carcinomas, odontogenic keratocysts, and multiple skeletal defects, e.g., frontal and temporoparietal bossing, bifurcated and splayed ribs, kyphoscoliosis, fusion of vertebrae, and cervicothoracic spina bifida. Genetic transmission is autosomal dominant.

Synonyms:

Gorlin Syndrome
Nevoid Basal Cell Carcinoma Syndrome
Nevus Syndrome, Basal Cell
Syndrome, Gorlin

Broader Topics:

Abnormalities, Multiple
Bone Diseases, Developmental
Carcinoma, Basal Cell
Neoplastic Syndromes, Hereditary
Odontogenic Cysts

Narrower Topics:

None

Possibly Related Topics:

List of topics based on word similarity